Case Report A RARE CASE OF HYPOGLOSSAL NERVE SCHWANNOMA ARISING AT THE LEVEL OF CAROTID BIFURCATION : A CASE REPORT
Authors
Dr. Sanjay Chatterjee, DR. SHRUTI JEYAKUMAR, Dr. ADITYA YAWALIKAR, Dr. SHIVANI DESAIFiles
Abstract
INTRODUCTION
Schwannomas are benign slow growing tumors that originate from the myelin sheath of the nerves; predominantly arising from the vestibular nerve in 90% of the cases. [1] Most schwannomas are sporadic and few are associated with NF1, Schwannomatosis, Carney’s complex etc. Among the non-vestibular schwannomas, only about 5% arise from the hypoglossal nerve; tumor composed purely of motor nerves. Most hypoglossal schwannomas are intracranial in location, followed by intracranial lesion with a secondary extracranial extension - most frequently in the parapharyngeal space. [2] Primary extracranial hypoglossal schwannoma is very rare. Among them, to this date, there are only 3 reported cases of hypoglossal nerve schwannoma located at the carotid bifurcation. [3,4,5] These tumors are often diagnosed late due to non-specific clinical history and examination findings. They are asymptomatic for many years and hence histopathology is the gold standard of diagnosis. [6] We hereby present a case of a 52 year old female who came with a slow growing painless mass in the right side of the neck.
References
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