A A Case of Severe Refractory Residual Sensory-neural Hearing loss in Guillain Barre Syndrome : An Unexplored Entity

Darshan Pandya; Satish Khadilkar; Riddhi Patel

doi:10.15713/ins.bhj.104

Authors

Darshan Pandya a:1:{s:5:"en_US";s:15:"Bombay Hospital";}
Satish Khadilkar
Riddhi Patel

DOI:

https://doi.org/10.15713/ins.bhj.104

Keywords:

Demyelination, Guillain-Barré Syndrome, sensorineural hearing loss, refractory

Abstract

Guillain-Barre syndrome is an acute areflexic rapidly progressive polyradiculoneuropathy with albumin-cytological dissociation. Cochlear nerve demyelination is a rare cause of hearing loss in GBS patients. Here, we are reporting a 28-year-old man with Guillain-Barré Syndrome (GBS) with Bilateral facial and acoustic neuropathy. On neurological examination, he had bifacial weakness, bilateral hypo-acusia, generalized areflexia and sensory motor deficits in the distal limbs. The nerve conduction tests showed the evidence of the demyelinating polyneuropathy. A pure tone audiogram showed bilateral sensorineural hearing loss of 40-50 dB. Thus, auditory dysfunction in GBS patients must be evaluated particularly in the setting of facial palsy.

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